[{"data":1,"prerenderedAt":-1},["ShallowReactive",2],{"health-study-detail:100589368":3},{"organization":4,"armGroups":7,"interventions":14,"overallOfficials":20,"centralContacts":27,"locations":33,"responsibleParty":58,"collaborators":60,"id":67,"slug":11,"hasResults":68,"nctId":69,"briefTitle":70,"officialTitle":71,"acronym":11,"eligibilityCriteria":72,"healthyVolunteers":68,"sex":73,"minAge":74,"maxAge":11,"enrollmentInfo":75,"targetDuration":11,"studyType":78,"phases":79,"briefSummary":81,"conditions":82,"keywords":11,"overallStatus":36,"whyStopped":11,"lastUpdateSubmitDate":87,"lastUpdatePostDateStruct":88,"startDateStruct":91,"completionDateStruct":93,"leadSponsor":95,"locationsCount":96},{"fullName":5,"class":6},"Sequitur Health Corp.","INDUSTRY",[8],{"label":9,"type":10,"description":11,"interventionNames":12},"Ammonia Device","EXPERIMENTAL",null,[13],"Diagnostic Test: Ammonia Study Device",[15],{"type":16,"name":17,"description":18,"armGroupLabels":19,"otherNames":11},"DIAGNOSTIC_TEST","Ammonia Study Device","Ammonia study device for capillary ammonia measurement",[9],[21,24],{"name":22,"affiliation":5,"role":23},"Marylaura L Thomas, Ph.D.","PRINCIPAL_INVESTIGATOR",{"name":25,"affiliation":5,"role":26},"Leslie F. Thomas, M.D.","STUDY_DIRECTOR",[28],{"name":29,"role":30,"phone":31,"phoneExt":11,"email":32},"Marylaura Thomas, Ph.D.","CONTACT","1-855-445-3889","info@sequiturhealth.com",[34],{"facility":35,"status":36,"city":37,"state":38,"zip":39,"country":40,"cosmosGeoPoint":41,"geoPoint":46,"contacts":47},"Oregon Health & Science University","RECRUITING","Portland","Oregon","97239-3098","United States",{"type":42,"coordinates":43},"Point",[44,45],-122.67621,45.52345,{"lat":45,"lon":44},[48,51,53,56],{"name":49,"role":30,"phone":50,"phoneExt":11,"email":11},"Amy C. Yang, M.D.","503-494-8307",{"name":52,"role":23,"phone":11,"phoneExt":11,"email":11},"Amy C Yang, M.D.",{"name":54,"role":55,"phone":11,"phoneExt":11,"email":11},"Brian Scottoline, M.D., Ph.D","SUB_INVESTIGATOR",{"name":57,"role":55,"phone":11,"phoneExt":11,"email":11},"Kimberly Kripps, M.D.",{"type":59,"investigatorFullName":11,"investigatorTitle":11,"investigatorAffiliation":11,"oldNameTitle":11,"oldOrganization":11},"SPONSOR",[61,64],{"name":62,"class":63},"Eunice Kennedy Shriver National Institute of Child Health and Human Development (NICHD)","NIH",{"name":65,"class":66},"Oregon Health and Science University","OTHER","100589368",false,"NCT06953505","At Home Ammonia Monitoring of Inborn Errors of Ammonia Metabolism","Pilot Study of At Home Ammonia Monitoring in Patients With an Inborn Error of Ammonia Metabolism","Inclusion Criteria:\n\n* Confirmed ammonia disorder such as\n\n  * Ornithine transcarbamylase deficiency\n  * Systemic primary carnitine deficiency\n  * Type I citrullinemia\n  * Argininosuccinic aciduria\n  * Isolated methylmalonic acidemia\n  * Type II citrullinemia\n  * Propionic acidemia\n  * Isovaleric acidemia\n  * Multiple acyl-CoA dehydrogenase deficiency\n  * Pyruvate carboxylase deficiency\n  * Argininemia (arginase deficiency)\n  * Carbamoyl phosphate synthase I deficiency\n  * Dihydrolipoamide dehydrogenase deficiency\n  * Lysinuric protein intolerance\n  * Hyperornithinemia-hyperammonemia-homocitrullinuria\n  * Carnitine-acylcarnitine translocase deficiency\n  * Carbonic anhydrase VA deficiency\n  * N-acetyl glutamate synthetase deficiency\n* English Literacy\n\nExclusion Criteria:\n\n* Incarcerated\n* Presence of a non-inborn error of metabolism medical condition associated with abnormal ammonia metabolism (e.g., end stage liver disease).\n* Unable to read in English","ALL","12 Years",{"count":76,"type":77},30,"ESTIMATED","INTERVENTIONAL",[80],"NA","The goal of this observational study is to learn if people with certain ammonia metabolism disorders will measure their ammonia levels at home.\n\nThe main question it aims to answer is:\n\n• Will participants measure their ammonia every day?\n\nParticipants will be asked to:\n\n* Attend two in-person study visits at the clinic.\n* Measure temperature, heart rate, and blood oxygen every day.\n* Complete a short survey every day.\n* Measure ammonia every day.",[83,84,85,86],"Urea Cycle Disorders","Organic Acidemias","Fatty Acid Oxidation Disorder","Ammonia; Metabolic Disorder","2026-05-21",{"date":89,"type":90},"2026-05-27","ACTUAL",{"date":92,"type":90},"2025-09-23",{"date":94,"type":77},"2027-08",{"name":5,"class":6},1]