About this trial

This is a prospective, real world, multicenter, registry of patients with pulmonary hypertension associated with interstitial lung disease (PH-ILD) and interstitial lung disease (ILD).

Eligibility criteria

Qualifiers

Adults aged 18 years or older

Idiopathic interstitial pneumonia, including idiopathic pulmonary fibrosis

Autoimmune ILD

Chronic hypersensitivity pneumonitis

Disqualifiers

Confirmed diagnosis of Group 1, 2, 4, or 5 PH

Confirmed diagnosis of Group 3 PH associated with lung diseases and or hypoxia other than fibrotic ILD, as outlined in Inclusion Criterion 2.

Patients receiving inhaled treprostinil (Yutrepia™) at Baseline. Patients receiving other forms of PH therapy will be eligible for enrollment.

Trial design

Treatments tested in this trial

  • Prospective study assessments

Treatment groups

900 Participants
are divided into 4 treatment groups

Locations

67
Puerto Rico
Auxilio Mutuo Hospital00968, GuaynaboPuerto Rico, Puerto Rico
United States
Alabama
University of Alabama at Birmingham35294, Birmingham United States
Arizona
Banner Health - University Medical Center Phoenix85006, Phoenix United States
California
Cedars-Sinai Medical Center90048, Los Angeles United States

Sponsors and collaborators

United Therapeutics

Lead sponsor